Lichen Myxedematosus: Atypical form and Therapeutic Success with Intravenous Immunoglobulin

Lichen Myxedematosus: Atypical form and Therapeutic Success with Intravenous Immunoglobulin

Lichen myxedematosus is a cutaneous mucinosis of idiopathic origin. According to Rongioletti’s classification, 2006, lichen myxedematosus is classified into three forms. The scleromyxedema or lichen myxedematosus sclerodermiform and generalized is a form of lichen myxedematosus characterized by numerous papules and areas of cutaneous hardening due to the deposition of mucin in association with ...

Acral persistent papular mucinosis and lichen myxedematosus.

Case for diagnosis. Lichen myxedematosus*

Scleromyxedema or lichen myxedematosus is a rare papular mucinosis of chronic and progressive course and unknown etiology. It is commonly associated with monoclonal gammopathy and may show extracutaneous manifestations, affecting the heart, lung, kidney, and nerves. The diagnosis is based on four criteria: generalized papular and sclerodermoid lesions; mucin deposition, fibroblast proliferation...

Atypical Lichen Myxedematosus: A Case with Remarkable Response to Low Dose Melphalan

A 41-year-old man was referred to our outpatient department with a diagnosis of urticaria with angioedema of 3 months duration. On examination, he had generalized coalescent waxy papules and diffuse periorbital swelling. Systemic examination was unremarkable except for limited finger flexion. Serum electrophoresis and thyroid function tests were normal. Histopathological examination showed norm...

Discrete ('acral nonpapular') localised lichen myxedematosus.

To cite: Reserva J, Marchalik R, Braniecki M. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/ bcr-2015-209462 DESCRIPTION Localised lichen myxedematosus (LM) is a chronic idiopathic papular mucinosis that can be divided into five subtypes: a discrete papular (DPLM) form, acral persistent papular mucinosis (APPM), papular mucinosis of infancy, a nodular form and selfh...